Jejunal-ileal atresia is a segmental atresia of the jejunum or the ileum. It is associated with malrotation and volvulus (25%) and cystic fibrosis (10%). Patients present within the first days of life with vomiting or a distended abdomen.

Multiple distended loops of bowel.

Barium enema demonstrates unused microcolon in a patient with distal ileal atresia.