Cephalocele refers to an extracranial extension or protrusion of intracranial structures through a congenital defect in the skull and dura mater. Cephaloceles are classified by their contents and by the location of the cranial defect through which the herniation occurs. The herniating neural tissues found within the external skin covered sac may include meninges, brain parenchyma and/or ventricles with choroid plexus, and vascular structures. Occipital encephaloceles are most frequent among white populations in Europe and North America.