CNS tumors are the most common solid malignancy of childhood. Tumors of the posterior fossa are more common in children than in adults. Posterior fossa tumors often present with obstructive hydrocephalus secondary to compression of the fourth ventricle. The differential diagnosis for posterior fossa tumors in children is limited with the most frequent being juvenile pilocytic astrocytoma, medulloblastoma, brainstem glioma, and ependymoma.