Proximal Femoral Focal Deficiency (PFFD) is a congenital disorder consisting of variable degrees of hypoplasia or absence of proximal portions of the femur. In its most devastating forms, the proximal femur as well as the femoral head and acetabulum may be absent. The patients will often present with a varus deformity in addition to the shortened limb. Associated findings in patients with PFFD include ipsilateral fibular hemimelia (absent fibula) and deformity of the foot.